Cargando…
Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability
Intellectual disability (ID) is a condition of significant limitation of cognitive functioning and adaptive behavior, with 50% of etiology attributed to genetic predisposition. We recruited two consanguineous Pakistani families manifesting severe ID and developmental delay. The probands were subject...
Autores principales: | , , , , , , , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2022
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9858807/ https://www.ncbi.nlm.nih.gov/pubmed/36672789 http://dx.doi.org/10.3390/genes14010048 |
_version_ | 1784874196322484224 |
---|---|
author | Asif, Maria Anayat, Maryam Tariq, Faiza Noureen, Tanzeela Din, Ghulam Naseer Ud Becker, Christian Becker, Kerstin Thiele, Holger Makhdoom, Ehtisham ul Haq Shaiq, Pakeeza Arzoo Baig, Shahid M. Nürnberg, Peter Hussain, Muhammad Sajid Raja, Ghazala Kaukab Abdullah, Uzma |
author_facet | Asif, Maria Anayat, Maryam Tariq, Faiza Noureen, Tanzeela Din, Ghulam Naseer Ud Becker, Christian Becker, Kerstin Thiele, Holger Makhdoom, Ehtisham ul Haq Shaiq, Pakeeza Arzoo Baig, Shahid M. Nürnberg, Peter Hussain, Muhammad Sajid Raja, Ghazala Kaukab Abdullah, Uzma |
author_sort | Asif, Maria |
collection | PubMed |
description | Intellectual disability (ID) is a condition of significant limitation of cognitive functioning and adaptive behavior, with 50% of etiology attributed to genetic predisposition. We recruited two consanguineous Pakistani families manifesting severe ID and developmental delay. The probands were subjected to whole exome sequencing (WES) and variants were further prioritized based on population frequency, predicted pathogenicity and functional relevance. The WES data analysis identified homozygous pathogenic variants in genes MBOAT7 and TRAPPC9. The pathogenicity of the variants was supported by co-segregation analysis and in silico tool. The findings of this study expand mutation spectrum and provide additional evidence to the role of MBOAT7 and TRAPPC9 in causation of ID. |
format | Online Article Text |
id | pubmed-9858807 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-98588072023-01-21 Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability Asif, Maria Anayat, Maryam Tariq, Faiza Noureen, Tanzeela Din, Ghulam Naseer Ud Becker, Christian Becker, Kerstin Thiele, Holger Makhdoom, Ehtisham ul Haq Shaiq, Pakeeza Arzoo Baig, Shahid M. Nürnberg, Peter Hussain, Muhammad Sajid Raja, Ghazala Kaukab Abdullah, Uzma Genes (Basel) Article Intellectual disability (ID) is a condition of significant limitation of cognitive functioning and adaptive behavior, with 50% of etiology attributed to genetic predisposition. We recruited two consanguineous Pakistani families manifesting severe ID and developmental delay. The probands were subjected to whole exome sequencing (WES) and variants were further prioritized based on population frequency, predicted pathogenicity and functional relevance. The WES data analysis identified homozygous pathogenic variants in genes MBOAT7 and TRAPPC9. The pathogenicity of the variants was supported by co-segregation analysis and in silico tool. The findings of this study expand mutation spectrum and provide additional evidence to the role of MBOAT7 and TRAPPC9 in causation of ID. MDPI 2022-12-23 /pmc/articles/PMC9858807/ /pubmed/36672789 http://dx.doi.org/10.3390/genes14010048 Text en © 2022 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Article Asif, Maria Anayat, Maryam Tariq, Faiza Noureen, Tanzeela Din, Ghulam Naseer Ud Becker, Christian Becker, Kerstin Thiele, Holger Makhdoom, Ehtisham ul Haq Shaiq, Pakeeza Arzoo Baig, Shahid M. Nürnberg, Peter Hussain, Muhammad Sajid Raja, Ghazala Kaukab Abdullah, Uzma Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title | Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title_full | Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title_fullStr | Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title_full_unstemmed | Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title_short | Whole-Exome Sequencing of Pakistani Consanguineous Families Identified Pathogenic Variants in Genes of Intellectual Disability |
title_sort | whole-exome sequencing of pakistani consanguineous families identified pathogenic variants in genes of intellectual disability |
topic | Article |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9858807/ https://www.ncbi.nlm.nih.gov/pubmed/36672789 http://dx.doi.org/10.3390/genes14010048 |
work_keys_str_mv | AT asifmaria wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT anayatmaryam wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT tariqfaiza wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT noureentanzeela wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT dinghulamnaseerud wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT beckerchristian wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT beckerkerstin wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT thieleholger wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT makhdoomehtishamulhaq wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT shaiqpakeezaarzoo wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT baigshahidm wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT nurnbergpeter wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT hussainmuhammadsajid wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT rajaghazalakaukab wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability AT abdullahuzma wholeexomesequencingofpakistaniconsanguineousfamiliesidentifiedpathogenicvariantsingenesofintellectualdisability |