Cargando…

Metastatic Adrenal PEComa: Case Report and Short Review of the Literature

PEComa has become a widely accepted entity, and increased recognition has led to descriptions of this tumor in a wide variety of anatomic sites, including the adrenal gland. PEComa (perivascular epithelioid cell tumor) is a mesenchymal tumor composed of perivascular cells, and the most frequent site...

Descripción completa

Detalles Bibliográficos
Autores principales: Battistella, Enrico, Pomba, Luca, Mirabella, Marica, Gregianin, Michele, Scapinello, Antonio, Volante, Marco, Toniato, Antonio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9866888/
https://www.ncbi.nlm.nih.gov/pubmed/36676773
http://dx.doi.org/10.3390/medicina59010149
_version_ 1784876204022562816
author Battistella, Enrico
Pomba, Luca
Mirabella, Marica
Gregianin, Michele
Scapinello, Antonio
Volante, Marco
Toniato, Antonio
author_facet Battistella, Enrico
Pomba, Luca
Mirabella, Marica
Gregianin, Michele
Scapinello, Antonio
Volante, Marco
Toniato, Antonio
author_sort Battistella, Enrico
collection PubMed
description PEComa has become a widely accepted entity, and increased recognition has led to descriptions of this tumor in a wide variety of anatomic sites, including the adrenal gland. PEComa (perivascular epithelioid cell tumor) is a mesenchymal tumor composed of perivascular cells, and the most frequent sites of PEComas are the uterus and retroperitoneum. The incidence is <1 per 1,000,000 people. We report a case of adrenal metastatic PEComa in a 63-year-old man discovered by a spontaneous hematoma of the rectus abdominis. In our case, PEComa of the adrenal gland was a significant diagnostic dilemma as the morphologic and immunophenotypic features of this neoplasm may easily be confused with those of other more commonly encountered lesions.
format Online
Article
Text
id pubmed-9866888
institution National Center for Biotechnology Information
language English
publishDate 2023
publisher MDPI
record_format MEDLINE/PubMed
spelling pubmed-98668882023-01-22 Metastatic Adrenal PEComa: Case Report and Short Review of the Literature Battistella, Enrico Pomba, Luca Mirabella, Marica Gregianin, Michele Scapinello, Antonio Volante, Marco Toniato, Antonio Medicina (Kaunas) Case Report PEComa has become a widely accepted entity, and increased recognition has led to descriptions of this tumor in a wide variety of anatomic sites, including the adrenal gland. PEComa (perivascular epithelioid cell tumor) is a mesenchymal tumor composed of perivascular cells, and the most frequent sites of PEComas are the uterus and retroperitoneum. The incidence is <1 per 1,000,000 people. We report a case of adrenal metastatic PEComa in a 63-year-old man discovered by a spontaneous hematoma of the rectus abdominis. In our case, PEComa of the adrenal gland was a significant diagnostic dilemma as the morphologic and immunophenotypic features of this neoplasm may easily be confused with those of other more commonly encountered lesions. MDPI 2023-01-11 /pmc/articles/PMC9866888/ /pubmed/36676773 http://dx.doi.org/10.3390/medicina59010149 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Battistella, Enrico
Pomba, Luca
Mirabella, Marica
Gregianin, Michele
Scapinello, Antonio
Volante, Marco
Toniato, Antonio
Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title_full Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title_fullStr Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title_full_unstemmed Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title_short Metastatic Adrenal PEComa: Case Report and Short Review of the Literature
title_sort metastatic adrenal pecoma: case report and short review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9866888/
https://www.ncbi.nlm.nih.gov/pubmed/36676773
http://dx.doi.org/10.3390/medicina59010149
work_keys_str_mv AT battistellaenrico metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT pombaluca metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT mirabellamarica metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT gregianinmichele metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT scapinelloantonio metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT volantemarco metastaticadrenalpecomacasereportandshortreviewoftheliterature
AT toniatoantonio metastaticadrenalpecomacasereportandshortreviewoftheliterature