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Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings

A perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm with distinctive perivascular epithelioid cells that usually demonstrates myomelanocytic differentiation. PEComas can arise in various organs and generally are benign. Uncommonly PEComas have been documented to be malignan...

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Detalles Bibliográficos
Autores principales: Dhaliwal, Kody, Marslender, Shannon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9873579/
https://www.ncbi.nlm.nih.gov/pubmed/36712190
http://dx.doi.org/10.1016/j.radcr.2022.11.042
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author Dhaliwal, Kody
Marslender, Shannon
author_facet Dhaliwal, Kody
Marslender, Shannon
author_sort Dhaliwal, Kody
collection PubMed
description A perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm with distinctive perivascular epithelioid cells that usually demonstrates myomelanocytic differentiation. PEComas can arise in various organs and generally are benign. Uncommonly PEComas have been documented to be malignant with metastasis most frequently to the lung, liver, lymph nodes, and bone. Here, we present the case of a 59-year-old male with a malignant retroperitoneal PEComa with confirmed metastasis to the femur and suspected metastasis to the liver and lung. The purpose of this case study is to present the progression and findings of a metastatic malignant PEComa.
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spelling pubmed-98735792023-01-26 Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings Dhaliwal, Kody Marslender, Shannon Radiol Case Rep Case Report A perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm with distinctive perivascular epithelioid cells that usually demonstrates myomelanocytic differentiation. PEComas can arise in various organs and generally are benign. Uncommonly PEComas have been documented to be malignant with metastasis most frequently to the lung, liver, lymph nodes, and bone. Here, we present the case of a 59-year-old male with a malignant retroperitoneal PEComa with confirmed metastasis to the femur and suspected metastasis to the liver and lung. The purpose of this case study is to present the progression and findings of a metastatic malignant PEComa. Elsevier 2023-01-22 /pmc/articles/PMC9873579/ /pubmed/36712190 http://dx.doi.org/10.1016/j.radcr.2022.11.042 Text en © 2023 Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Dhaliwal, Kody
Marslender, Shannon
Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title_full Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title_fullStr Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title_full_unstemmed Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title_short Malignant retroperitoneal PEComa: A case report with emphasis on radiological findings
title_sort malignant retroperitoneal pecoma: a case report with emphasis on radiological findings
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9873579/
https://www.ncbi.nlm.nih.gov/pubmed/36712190
http://dx.doi.org/10.1016/j.radcr.2022.11.042
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