Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature

Primary renal primitive neuroectodermal tumors (PNET) are an extremely rare entity. The tumor is very aggressive presenting with metastasis and carries a dismal prognosis. We describe the case of renal PNET in an 11-year-old boy with a solid cystic lesion in the right kidney with a thrombus in the i...

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Autores principales: More, Miloni, Jayaraman, Dhaarani, Babu, Ramesh, Rajasekaran, Banukeerthana, Jaison, Jensy, Scott, Julius Xavier
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2022
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9878518/
https://www.ncbi.nlm.nih.gov/pubmed/36714469
http://dx.doi.org/10.4103/jiaps.jiaps_50_22
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author More, Miloni
Jayaraman, Dhaarani
Babu, Ramesh
Rajasekaran, Banukeerthana
Jaison, Jensy
Scott, Julius Xavier
author_facet More, Miloni
Jayaraman, Dhaarani
Babu, Ramesh
Rajasekaran, Banukeerthana
Jaison, Jensy
Scott, Julius Xavier
author_sort More, Miloni
collection PubMed
description Primary renal primitive neuroectodermal tumors (PNET) are an extremely rare entity. The tumor is very aggressive presenting with metastasis and carries a dismal prognosis. We describe the case of renal PNET in an 11-year-old boy with a solid cystic lesion in the right kidney with a thrombus in the inferior vena cava and lung nodules, mimicking Wilms' tumor.
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spelling pubmed-98785182023-01-27 Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature More, Miloni Jayaraman, Dhaarani Babu, Ramesh Rajasekaran, Banukeerthana Jaison, Jensy Scott, Julius Xavier J Indian Assoc Pediatr Surg Case Report Primary renal primitive neuroectodermal tumors (PNET) are an extremely rare entity. The tumor is very aggressive presenting with metastasis and carries a dismal prognosis. We describe the case of renal PNET in an 11-year-old boy with a solid cystic lesion in the right kidney with a thrombus in the inferior vena cava and lung nodules, mimicking Wilms' tumor. Wolters Kluwer - Medknow 2022 2022-11-14 /pmc/articles/PMC9878518/ /pubmed/36714469 http://dx.doi.org/10.4103/jiaps.jiaps_50_22 Text en Copyright: © 2022 Journal of Indian Association of Pediatric Surgeons https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
More, Miloni
Jayaraman, Dhaarani
Babu, Ramesh
Rajasekaran, Banukeerthana
Jaison, Jensy
Scott, Julius Xavier
Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title_full Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title_fullStr Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title_full_unstemmed Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title_short Renal Primitive Neuroectodermal Tumor Mimicking Wilms' Tumor in a Young Boy: A Case Report of a Rare Entity with Review of the Literature
title_sort renal primitive neuroectodermal tumor mimicking wilms' tumor in a young boy: a case report of a rare entity with review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9878518/
https://www.ncbi.nlm.nih.gov/pubmed/36714469
http://dx.doi.org/10.4103/jiaps.jiaps_50_22
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