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Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature
Pancreatoblastoma, an orphan disease, is the most common malignant epithelial neoplasm of the pancreas in children. With vague clinical features, diagnosis is made by radiological suggestions and histopathology. The presence of metastatic disease and inoperable/incomplete excision remains the poor p...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Wolters Kluwer - Medknow
2022
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9878534/ https://www.ncbi.nlm.nih.gov/pubmed/36714488 http://dx.doi.org/10.4103/jiaps.jiaps_4_22 |
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author | Jayaraman, Dhaarani John, Arockia Bose, Jagadesh Chandra Venkitaraman, Balasubramanian Shalini, Sai Murali, Arunan |
author_facet | Jayaraman, Dhaarani John, Arockia Bose, Jagadesh Chandra Venkitaraman, Balasubramanian Shalini, Sai Murali, Arunan |
author_sort | Jayaraman, Dhaarani |
collection | PubMed |
description | Pancreatoblastoma, an orphan disease, is the most common malignant epithelial neoplasm of the pancreas in children. With vague clinical features, diagnosis is made by radiological suggestions and histopathology. The presence of metastatic disease and inoperable/incomplete excision remains the poor prognostic markers. We present a rare instance of an adolescent who has survived metastatic pancreatoblastoma after neoadjuvant chemoreduction/complete surgical excision. |
format | Online Article Text |
id | pubmed-9878534 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2022 |
publisher | Wolters Kluwer - Medknow |
record_format | MEDLINE/PubMed |
spelling | pubmed-98785342023-01-27 Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature Jayaraman, Dhaarani John, Arockia Bose, Jagadesh Chandra Venkitaraman, Balasubramanian Shalini, Sai Murali, Arunan J Indian Assoc Pediatr Surg Case Report Pancreatoblastoma, an orphan disease, is the most common malignant epithelial neoplasm of the pancreas in children. With vague clinical features, diagnosis is made by radiological suggestions and histopathology. The presence of metastatic disease and inoperable/incomplete excision remains the poor prognostic markers. We present a rare instance of an adolescent who has survived metastatic pancreatoblastoma after neoadjuvant chemoreduction/complete surgical excision. Wolters Kluwer - Medknow 2022 2022-11-14 /pmc/articles/PMC9878534/ /pubmed/36714488 http://dx.doi.org/10.4103/jiaps.jiaps_4_22 Text en Copyright: © 2022 Journal of Indian Association of Pediatric Surgeons https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Jayaraman, Dhaarani John, Arockia Bose, Jagadesh Chandra Venkitaraman, Balasubramanian Shalini, Sai Murali, Arunan Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title | Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title_full | Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title_fullStr | Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title_full_unstemmed | Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title_short | Successful Outcome of Metastatic Pancreatoblastoma in an Adolescent: A Case Report and Review of the Literature |
title_sort | successful outcome of metastatic pancreatoblastoma in an adolescent: a case report and review of the literature |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9878534/ https://www.ncbi.nlm.nih.gov/pubmed/36714488 http://dx.doi.org/10.4103/jiaps.jiaps_4_22 |
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