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Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child
Acute pandysautonomia-associated distal esophageal spasm is a rare disease with an unclear etiology. Here, we describe a 12-year-old boy with an acute pandysautonomia-associated distal esophageal spasm who was treated using a peroral endoscopic myotomy (POEM). The patient's clinical features in...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9887313/ https://www.ncbi.nlm.nih.gov/pubmed/36733769 http://dx.doi.org/10.3389/fped.2022.935915 |
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author | Zhang, Hanhua Chi, Biyun Wang, Fengfan Shao, Pei Liu, Huanyu Fang, Ying |
author_facet | Zhang, Hanhua Chi, Biyun Wang, Fengfan Shao, Pei Liu, Huanyu Fang, Ying |
author_sort | Zhang, Hanhua |
collection | PubMed |
description | Acute pandysautonomia-associated distal esophageal spasm is a rare disease with an unclear etiology. Here, we describe a 12-year-old boy with an acute pandysautonomia-associated distal esophageal spasm who was treated using a peroral endoscopic myotomy (POEM). The patient's clinical features included recurrent dysphagia, nausea, vomiting, growth retardation, and signs of autonomic nerve dysfunction (e.g., a decreased production of tears and sweat, and an increased production of saliva). Signs of the distal esophageal spasm were visible in upper gastrointestinal radiography, endoscopy, and high-resolution esophageal manometry. After the POEM, the patient exhibited improvements in nausea and vomiting, and his dysphagia symptoms were relieved by the 6-month follow-up visit. However, the patient's neurological problems persisted. The satisfactory short-term clinical responses in our patient suggest that POEM is feasible, safe, and effective for the treatment of acute pandysautonomia-associated distal esophageal spasms in children. |
format | Online Article Text |
id | pubmed-9887313 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Frontiers Media S.A. |
record_format | MEDLINE/PubMed |
spelling | pubmed-98873132023-02-01 Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child Zhang, Hanhua Chi, Biyun Wang, Fengfan Shao, Pei Liu, Huanyu Fang, Ying Front Pediatr Pediatrics Acute pandysautonomia-associated distal esophageal spasm is a rare disease with an unclear etiology. Here, we describe a 12-year-old boy with an acute pandysautonomia-associated distal esophageal spasm who was treated using a peroral endoscopic myotomy (POEM). The patient's clinical features included recurrent dysphagia, nausea, vomiting, growth retardation, and signs of autonomic nerve dysfunction (e.g., a decreased production of tears and sweat, and an increased production of saliva). Signs of the distal esophageal spasm were visible in upper gastrointestinal radiography, endoscopy, and high-resolution esophageal manometry. After the POEM, the patient exhibited improvements in nausea and vomiting, and his dysphagia symptoms were relieved by the 6-month follow-up visit. However, the patient's neurological problems persisted. The satisfactory short-term clinical responses in our patient suggest that POEM is feasible, safe, and effective for the treatment of acute pandysautonomia-associated distal esophageal spasms in children. Frontiers Media S.A. 2023-01-17 /pmc/articles/PMC9887313/ /pubmed/36733769 http://dx.doi.org/10.3389/fped.2022.935915 Text en © 2023 Zhang, Chi, Wang, Shao, Liu and Fang. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY) (https://creativecommons.org/licenses/by/4.0/) . The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms. |
spellingShingle | Pediatrics Zhang, Hanhua Chi, Biyun Wang, Fengfan Shao, Pei Liu, Huanyu Fang, Ying Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title | Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title_full | Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title_fullStr | Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title_full_unstemmed | Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title_short | Case report: Peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
title_sort | case report: peroral endoscopic myotomy for acute pandysautonomia-associated distal esophageal spasm in a child |
topic | Pediatrics |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9887313/ https://www.ncbi.nlm.nih.gov/pubmed/36733769 http://dx.doi.org/10.3389/fped.2022.935915 |
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