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Fulminant Viral Hepatitis in Two Siblings with Inherited IL-10RB Deficiency

Fulminant viral hepatitis (FVH) caused by hepatitis A virus (HAV) is a life-threatening disease that typically strikes otherwise healthy individuals. The only known genetic etiology of FVH is inherited IL-18BP deficiency, which unleashes IL-18-dependent lymphocyte cytotoxicity and IFN-γ production....

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Detalles Bibliográficos
Autores principales:	Korol, Cecilia B., Belkaya, Serkan, Alsohime, Fahad, Lorenzo, Lazaro, Boisson-Dupuis, Stéphanie, Brancale, Joseph, Neehus, Anna-Lena, Vilarinho, Silvia, Zobaida, Alsum, Halwani, Rabih, Al-Muhsen, Saleh, Casanova, Jean-Laurent, Jouanguy, Emmanuelle
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Springer US 2022
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9892130/ https://www.ncbi.nlm.nih.gov/pubmed/36308662 http://dx.doi.org/10.1007/s10875-022-01376-5

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