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Challenges in Anesthesia in Wilson’s Disease: A Systematic Review of the Existing Literature

Wilson’s disease (WD) is a disorder of copper metabolism presenting with a wide variety of organ dysfunctions affecting predominantly the neurological, hepatic, and hematological systems. Due to its multi-systemic nature, administering anesthesia to a patient with WD is challenging and requires an i...

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Detalles Bibliográficos
Autores principales: Aravindan, Ajisha, Shiva Priya, Kandukuri, Roy Chowdhury, Sumit, Datta, Priyankar K
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9896130/
https://www.ncbi.nlm.nih.gov/pubmed/36741662
http://dx.doi.org/10.7759/cureus.33334
Descripción
Sumario:Wilson’s disease (WD) is a disorder of copper metabolism presenting with a wide variety of organ dysfunctions affecting predominantly the neurological, hepatic, and hematological systems. Due to its multi-systemic nature, administering anesthesia to a patient with WD is challenging and requires an in-depth knowledge of the disease pathophysiology. A systematic search for literature pertaining to the anesthetic management of patients with WD yielded 19 case reports, which we have included in this review to explore and summarize peri-operative concerns and the safe anesthesia practices in this condition.