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Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review

BACKGROUND: Turner syndrome is a rare systemic disease and a significant proportion of these patients experience aortic coarctation. Selection of optimal therapy for aortic coarctation in patients with Turner syndrome is difficult due to the pathologic change of the systemic vessel. CASE PRESENTATIO...

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Autores principales: Lin, Yuese, Zhu, Ling, Li, Xuandi, Ba, Hongjun, He, Xiufang, Li, Shujuan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9909388/
https://www.ncbi.nlm.nih.gov/pubmed/36776680
http://dx.doi.org/10.3389/fped.2022.1041728
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author Lin, Yuese
Zhu, Ling
Li, Xuandi
Ba, Hongjun
He, Xiufang
Li, Shujuan
author_facet Lin, Yuese
Zhu, Ling
Li, Xuandi
Ba, Hongjun
He, Xiufang
Li, Shujuan
author_sort Lin, Yuese
collection PubMed
description BACKGROUND: Turner syndrome is a rare systemic disease and a significant proportion of these patients experience aortic coarctation. Selection of optimal therapy for aortic coarctation in patients with Turner syndrome is difficult due to the pathologic change of the systemic vessel. CASE PRESENTATION: We report one successful case of covered stent implantation for the treatment of severe native coarctation of the aorta in a 15-year-old patient with Turner syndrome weighing 36 kg. A covered stent was implanted in this patient. After the stent implantation, the peak systolic pressure gradient immediately decreased from 48 mmHg to 14 mmHg. The aortic diameter at the coarctation site increased from 3 mm to 10 mm after stenting. A femoral arterial complication occurred in this case, and we stabilized the situation finally. RESULTS: During a follow-up of 3 years, no restenosis of aortic coarctation was observed and the patient no longer experienced hypertension. The dissection of the right femoral artery remained stable. CONCLUSION: A covered stent implantation for severe aortic coarctation in patients with Turner syndrome could be safe and effective. However, caution should be taken when using the technique to prevent complications.
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spelling pubmed-99093882023-02-10 Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review Lin, Yuese Zhu, Ling Li, Xuandi Ba, Hongjun He, Xiufang Li, Shujuan Front Pediatr Pediatrics BACKGROUND: Turner syndrome is a rare systemic disease and a significant proportion of these patients experience aortic coarctation. Selection of optimal therapy for aortic coarctation in patients with Turner syndrome is difficult due to the pathologic change of the systemic vessel. CASE PRESENTATION: We report one successful case of covered stent implantation for the treatment of severe native coarctation of the aorta in a 15-year-old patient with Turner syndrome weighing 36 kg. A covered stent was implanted in this patient. After the stent implantation, the peak systolic pressure gradient immediately decreased from 48 mmHg to 14 mmHg. The aortic diameter at the coarctation site increased from 3 mm to 10 mm after stenting. A femoral arterial complication occurred in this case, and we stabilized the situation finally. RESULTS: During a follow-up of 3 years, no restenosis of aortic coarctation was observed and the patient no longer experienced hypertension. The dissection of the right femoral artery remained stable. CONCLUSION: A covered stent implantation for severe aortic coarctation in patients with Turner syndrome could be safe and effective. However, caution should be taken when using the technique to prevent complications. Frontiers Media S.A. 2023-01-26 /pmc/articles/PMC9909388/ /pubmed/36776680 http://dx.doi.org/10.3389/fped.2022.1041728 Text en © 2023 Lin, Zhu, Li, Ba, He and Li. https://creativecommons.org/licenses/by/4.0/This is an open-access article distributed under the terms of the Creative Commons Attribution License (CC BY) (https://creativecommons.org/licenses/by/4.0/) . The use, distribution or reproduction in other forums is permitted, provided the original author(s) and the copyright owner(s) are credited and that the original publication in this journal is cited, in accordance with accepted academic practice. No use, distribution or reproduction is permitted which does not comply with these terms.
spellingShingle Pediatrics
Lin, Yuese
Zhu, Ling
Li, Xuandi
Ba, Hongjun
He, Xiufang
Li, Shujuan
Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title_full Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title_fullStr Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title_full_unstemmed Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title_short Stent implantation in severe aortic coarctation in a pediatric patient with Turner syndrome: Case report and literature review
title_sort stent implantation in severe aortic coarctation in a pediatric patient with turner syndrome: case report and literature review
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9909388/
https://www.ncbi.nlm.nih.gov/pubmed/36776680
http://dx.doi.org/10.3389/fped.2022.1041728
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