The world of rare interstitial lung diseases

The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and therapy usually pose challenges. This review describes a selection of rare and ultrarare ILDs including pulmonary alveolar proteinosis, pulmonary alveolar microlithiasis and pleuroparenchymal fibroelastosis. In...

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Autores principales: Buschulte, Katharina, Cottin, Vincent, Wijsenbeek, Marlies, Kreuter, Michael, Diesler, Rémi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2023
Materias:
Series
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9910344/
https://www.ncbi.nlm.nih.gov/pubmed/36754433
http://dx.doi.org/10.1183/16000617.0161-2022
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author Buschulte, Katharina
Cottin, Vincent
Wijsenbeek, Marlies
Kreuter, Michael
Diesler, Rémi
author_facet Buschulte, Katharina
Cottin, Vincent
Wijsenbeek, Marlies
Kreuter, Michael
Diesler, Rémi
author_sort Buschulte, Katharina
collection PubMed
description The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and therapy usually pose challenges. This review describes a selection of rare and ultrarare ILDs including pulmonary alveolar proteinosis, pulmonary alveolar microlithiasis and pleuroparenchymal fibroelastosis. In addition, monogenic ILDs or ILDs in congenital syndromes and various multiple cystic lung diseases will be discussed. All these conditions are part of the scope of the European Reference Network on rare respiratory diseases (ERN-LUNG). Epidemiology, pathogenesis, diagnostics and treatment of each disease are presented.
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spelling pubmed-99103442023-02-13 The world of rare interstitial lung diseases Buschulte, Katharina Cottin, Vincent Wijsenbeek, Marlies Kreuter, Michael Diesler, Rémi Eur Respir Rev Series The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and therapy usually pose challenges. This review describes a selection of rare and ultrarare ILDs including pulmonary alveolar proteinosis, pulmonary alveolar microlithiasis and pleuroparenchymal fibroelastosis. In addition, monogenic ILDs or ILDs in congenital syndromes and various multiple cystic lung diseases will be discussed. All these conditions are part of the scope of the European Reference Network on rare respiratory diseases (ERN-LUNG). Epidemiology, pathogenesis, diagnostics and treatment of each disease are presented. European Respiratory Society 2023-02-08 /pmc/articles/PMC9910344/ /pubmed/36754433 http://dx.doi.org/10.1183/16000617.0161-2022 Text en Copyright ©The authors 2023 https://creativecommons.org/licenses/by-nc/4.0/This version is distributed under the terms of the Creative Commons Attribution Non-Commercial Licence 4.0. For commercial reproduction rights and permissions contact permissions@ersnet.org (mailto:permissions@ersnet.org)
spellingShingle Series
Buschulte, Katharina
Cottin, Vincent
Wijsenbeek, Marlies
Kreuter, Michael
Diesler, Rémi
The world of rare interstitial lung diseases
title The world of rare interstitial lung diseases
title_full The world of rare interstitial lung diseases
title_fullStr The world of rare interstitial lung diseases
title_full_unstemmed The world of rare interstitial lung diseases
title_short The world of rare interstitial lung diseases
title_sort world of rare interstitial lung diseases
topic Series
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9910344/
https://www.ncbi.nlm.nih.gov/pubmed/36754433
http://dx.doi.org/10.1183/16000617.0161-2022
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