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Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect

Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is...

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Autores principales: Adu‐Boakye, Yaw, Amponsah, Gordon Manu, Andoh, Henry Kofi, Gyan, Kwadwo Faka, Wiafe, Yaw Amo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9913180/
https://www.ncbi.nlm.nih.gov/pubmed/36789326
http://dx.doi.org/10.1002/ccr3.6939
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author Adu‐Boakye, Yaw
Amponsah, Gordon Manu
Andoh, Henry Kofi
Gyan, Kwadwo Faka
Wiafe, Yaw Amo
author_facet Adu‐Boakye, Yaw
Amponsah, Gordon Manu
Andoh, Henry Kofi
Gyan, Kwadwo Faka
Wiafe, Yaw Amo
author_sort Adu‐Boakye, Yaw
collection PubMed
description Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is usually poor, with conservative treatment if the diagnosis is late and the patient develops heart failure and pulmonary hypertension. Although rheumatic heart disease (RHD) and congenital heart disease are prevalent in Ghana, cases of LS are not reported. Here, we report the case of a 45‐year‐old woman with rheumatic mitral valve stenosis and an exceptionally large ASD with bidirectional flow who was diagnosed with LS and treated conservatively for heart failure at a cardiology clinic in Ghana.
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spelling pubmed-99131802023-02-13 Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect Adu‐Boakye, Yaw Amponsah, Gordon Manu Andoh, Henry Kofi Gyan, Kwadwo Faka Wiafe, Yaw Amo Clin Case Rep Case Report Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is usually poor, with conservative treatment if the diagnosis is late and the patient develops heart failure and pulmonary hypertension. Although rheumatic heart disease (RHD) and congenital heart disease are prevalent in Ghana, cases of LS are not reported. Here, we report the case of a 45‐year‐old woman with rheumatic mitral valve stenosis and an exceptionally large ASD with bidirectional flow who was diagnosed with LS and treated conservatively for heart failure at a cardiology clinic in Ghana. John Wiley and Sons Inc. 2023-02-10 /pmc/articles/PMC9913180/ /pubmed/36789326 http://dx.doi.org/10.1002/ccr3.6939 Text en © 2023 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Adu‐Boakye, Yaw
Amponsah, Gordon Manu
Andoh, Henry Kofi
Gyan, Kwadwo Faka
Wiafe, Yaw Amo
Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title_full Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title_fullStr Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title_full_unstemmed Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title_short Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
title_sort lutembacher syndrome in a middle‐aged woman in ghana with an extremely large atrial septal defect
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9913180/
https://www.ncbi.nlm.nih.gov/pubmed/36789326
http://dx.doi.org/10.1002/ccr3.6939
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