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Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect
Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9913180/ https://www.ncbi.nlm.nih.gov/pubmed/36789326 http://dx.doi.org/10.1002/ccr3.6939 |
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author | Adu‐Boakye, Yaw Amponsah, Gordon Manu Andoh, Henry Kofi Gyan, Kwadwo Faka Wiafe, Yaw Amo |
author_facet | Adu‐Boakye, Yaw Amponsah, Gordon Manu Andoh, Henry Kofi Gyan, Kwadwo Faka Wiafe, Yaw Amo |
author_sort | Adu‐Boakye, Yaw |
collection | PubMed |
description | Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is usually poor, with conservative treatment if the diagnosis is late and the patient develops heart failure and pulmonary hypertension. Although rheumatic heart disease (RHD) and congenital heart disease are prevalent in Ghana, cases of LS are not reported. Here, we report the case of a 45‐year‐old woman with rheumatic mitral valve stenosis and an exceptionally large ASD with bidirectional flow who was diagnosed with LS and treated conservatively for heart failure at a cardiology clinic in Ghana. |
format | Online Article Text |
id | pubmed-9913180 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-99131802023-02-13 Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect Adu‐Boakye, Yaw Amponsah, Gordon Manu Andoh, Henry Kofi Gyan, Kwadwo Faka Wiafe, Yaw Amo Clin Case Rep Case Report Lutembacher syndrome (LS) is a rare heart disorder characterized by a congenital or acquired combination of the atrial septal defect (ASD) and mitral stenosis. In LS, patients may be asymptomatic for years, but early detection and treatment result in a better prognosis. In contrast, the prognosis is usually poor, with conservative treatment if the diagnosis is late and the patient develops heart failure and pulmonary hypertension. Although rheumatic heart disease (RHD) and congenital heart disease are prevalent in Ghana, cases of LS are not reported. Here, we report the case of a 45‐year‐old woman with rheumatic mitral valve stenosis and an exceptionally large ASD with bidirectional flow who was diagnosed with LS and treated conservatively for heart failure at a cardiology clinic in Ghana. John Wiley and Sons Inc. 2023-02-10 /pmc/articles/PMC9913180/ /pubmed/36789326 http://dx.doi.org/10.1002/ccr3.6939 Text en © 2023 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Adu‐Boakye, Yaw Amponsah, Gordon Manu Andoh, Henry Kofi Gyan, Kwadwo Faka Wiafe, Yaw Amo Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title | Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title_full | Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title_fullStr | Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title_full_unstemmed | Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title_short | Lutembacher syndrome in a middle‐aged woman in Ghana with an extremely large atrial septal defect |
title_sort | lutembacher syndrome in a middle‐aged woman in ghana with an extremely large atrial septal defect |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9913180/ https://www.ncbi.nlm.nih.gov/pubmed/36789326 http://dx.doi.org/10.1002/ccr3.6939 |
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