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Tofacitinib Is an Effective Treatment for Refractory Scleromyositis Associated With Anti-PM/Scl

Scleromyositis is a rare autoimmune disease characterized by overlapping scleroderma and myositis. This case report discusses the presentation and management of a 28-year-old male with scleromyositis presenting with myositis, arthritis, Raynaud’s phenomenon, refractory calcinosis, interstitial lung...

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Detalles Bibliográficos
Autores principales: Álvarez Troncoso, Jorge, Nuño González, Almudena, Martínez Robles, Elena, Sorriguieta Torre, Raquel, Robles Marhuenda, Ángel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9947514/
https://www.ncbi.nlm.nih.gov/pubmed/36843820
http://dx.doi.org/10.7759/cureus.34125
Descripción
Sumario:Scleromyositis is a rare autoimmune disease characterized by overlapping scleroderma and myositis. This case report discusses the presentation and management of a 28-year-old male with scleromyositis presenting with myositis, arthritis, Raynaud’s phenomenon, refractory calcinosis, interstitial lung disease, and myocarditis. This case highlights key points in the systematic approach to immunosuppressive treatment and proposes a novel therapeutic option.