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A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures

The diagnosis of vanishing gastroschisis is made when in the presence of a full-thickness intrauterine abdominal wall defect the eviscerated loops are incarcerated in the fascial interruption. Four types of vanishing gastroschisis are described (A–D). We report on the case of a newborn with a vanish...

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Autores principales: Guanà, Riccardo, Marocco, Lucia, Garofalo, Salvatore, Zambaiti, Elisa, Pane, Alessandro, Scottoni, Federico, Fusaro, Fabio, Perucca, Giulia, Gennari, Fabrizio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9989415/
https://www.ncbi.nlm.nih.gov/pubmed/36896328
http://dx.doi.org/10.1177/2050313X231157490
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author Guanà, Riccardo
Marocco, Lucia
Garofalo, Salvatore
Zambaiti, Elisa
Pane, Alessandro
Scottoni, Federico
Fusaro, Fabio
Perucca, Giulia
Gennari, Fabrizio
author_facet Guanà, Riccardo
Marocco, Lucia
Garofalo, Salvatore
Zambaiti, Elisa
Pane, Alessandro
Scottoni, Federico
Fusaro, Fabio
Perucca, Giulia
Gennari, Fabrizio
author_sort Guanà, Riccardo
collection PubMed
description The diagnosis of vanishing gastroschisis is made when in the presence of a full-thickness intrauterine abdominal wall defect the eviscerated loops are incarcerated in the fascial interruption. Four types of vanishing gastroschisis are described (A–D). We report on the case of a newborn with a vanishing gastroschisis-D. Gastroschisis was diagnosed at the 19th week of gestation, confirmed at the 30th, when the herniated loops previously visible to the right of the funiculus were no longer visualized. At the 32nd week, delivery was induced. The neonate weighed 1600 g, and the abdomen was distended, free from skin defects. On surgical exploration, the jejunum was 13 cm in length, with a blind ending. The post-atretic intestine measured 22 cm. A jejunostomy and a colostomy were built. The child received total parenteral nutrition for 13 months due to short bowel syndrome and was then subjected to intestinal lengthening procedure when she was 18 months old. Vanishing gastroschisis is a rare entity with a worse prognosis of the “classic” gastroschisis.
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spelling pubmed-99894152023-03-08 A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures Guanà, Riccardo Marocco, Lucia Garofalo, Salvatore Zambaiti, Elisa Pane, Alessandro Scottoni, Federico Fusaro, Fabio Perucca, Giulia Gennari, Fabrizio SAGE Open Med Case Rep Case Report The diagnosis of vanishing gastroschisis is made when in the presence of a full-thickness intrauterine abdominal wall defect the eviscerated loops are incarcerated in the fascial interruption. Four types of vanishing gastroschisis are described (A–D). We report on the case of a newborn with a vanishing gastroschisis-D. Gastroschisis was diagnosed at the 19th week of gestation, confirmed at the 30th, when the herniated loops previously visible to the right of the funiculus were no longer visualized. At the 32nd week, delivery was induced. The neonate weighed 1600 g, and the abdomen was distended, free from skin defects. On surgical exploration, the jejunum was 13 cm in length, with a blind ending. The post-atretic intestine measured 22 cm. A jejunostomy and a colostomy were built. The child received total parenteral nutrition for 13 months due to short bowel syndrome and was then subjected to intestinal lengthening procedure when she was 18 months old. Vanishing gastroschisis is a rare entity with a worse prognosis of the “classic” gastroschisis. SAGE Publications 2023-03-04 /pmc/articles/PMC9989415/ /pubmed/36896328 http://dx.doi.org/10.1177/2050313X231157490 Text en © The Author(s) 2023 https://creativecommons.org/licenses/by-nc/4.0/This article is distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 License (https://creativecommons.org/licenses/by-nc/4.0/) which permits non-commercial use, reproduction and distribution of the work without further permission provided the original work is attributed as specified on the SAGE and Open Access page (https://us.sagepub.com/en-us/nam/open-access-at-sage).
spellingShingle Case Report
Guanà, Riccardo
Marocco, Lucia
Garofalo, Salvatore
Zambaiti, Elisa
Pane, Alessandro
Scottoni, Federico
Fusaro, Fabio
Perucca, Giulia
Gennari, Fabrizio
A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title_full A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title_fullStr A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title_full_unstemmed A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title_short A case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
title_sort case of vanishing gastroschisis with short bowel syndrome treated by total parenteral nutrition and intestinal lengthening procedures
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9989415/
https://www.ncbi.nlm.nih.gov/pubmed/36896328
http://dx.doi.org/10.1177/2050313X231157490
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