Cargando…

Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation

Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with ot...

Descripción completa

Detalles Bibliográficos
Autores principales: Gebremariam, Dawit Seyoum, Miruts, Asmamaw, Desta, Kibrom Gebreselassie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9994661/
https://www.ncbi.nlm.nih.gov/pubmed/36910043
http://dx.doi.org/10.2147/PHMT.S397462
_version_ 1784902661056757760
author Gebremariam, Dawit Seyoum
Miruts, Asmamaw
Desta, Kibrom Gebreselassie
author_facet Gebremariam, Dawit Seyoum
Miruts, Asmamaw
Desta, Kibrom Gebreselassie
author_sort Gebremariam, Dawit Seyoum
collection PubMed
description Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with other syndromes. Fetal sonographic diagnosis of this defect is possible, but less practiced. After birth, this defect can be easily diagnosed clinically because of the presence of paradoxical chest wall movement. The flexibility of the thorax is maximal and compression of the underlying structures is minimal during the neonatal and early infancy period, and this period is the preferred time for surgical repair. We report a 39-day-old infant who presented with an isolated V-shaped inferior sternal cleft, its surgical primary closure, and postoperative course.
format Online
Article
Text
id pubmed-9994661
institution National Center for Biotechnology Information
language English
publishDate 2023
publisher Dove
record_format MEDLINE/PubMed
spelling pubmed-99946612023-03-09 Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation Gebremariam, Dawit Seyoum Miruts, Asmamaw Desta, Kibrom Gebreselassie Pediatric Health Med Ther Case Report Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with other syndromes. Fetal sonographic diagnosis of this defect is possible, but less practiced. After birth, this defect can be easily diagnosed clinically because of the presence of paradoxical chest wall movement. The flexibility of the thorax is maximal and compression of the underlying structures is minimal during the neonatal and early infancy period, and this period is the preferred time for surgical repair. We report a 39-day-old infant who presented with an isolated V-shaped inferior sternal cleft, its surgical primary closure, and postoperative course. Dove 2023-03-04 /pmc/articles/PMC9994661/ /pubmed/36910043 http://dx.doi.org/10.2147/PHMT.S397462 Text en © 2023 Gebremariam et al. https://creativecommons.org/licenses/by-nc/3.0/This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/ (https://creativecommons.org/licenses/by-nc/3.0/) ). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php).
spellingShingle Case Report
Gebremariam, Dawit Seyoum
Miruts, Asmamaw
Desta, Kibrom Gebreselassie
Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title_full Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title_fullStr Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title_full_unstemmed Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title_short Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
title_sort isolated v-shaped sternal cleft — a rare chest wall malformation
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9994661/
https://www.ncbi.nlm.nih.gov/pubmed/36910043
http://dx.doi.org/10.2147/PHMT.S397462
work_keys_str_mv AT gebremariamdawitseyoum isolatedvshapedsternalcleftararechestwallmalformation
AT mirutsasmamaw isolatedvshapedsternalcleftararechestwallmalformation
AT destakibromgebreselassie isolatedvshapedsternalcleftararechestwallmalformation