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Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation
Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with ot...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Dove
2023
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9994661/ https://www.ncbi.nlm.nih.gov/pubmed/36910043 http://dx.doi.org/10.2147/PHMT.S397462 |
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author | Gebremariam, Dawit Seyoum Miruts, Asmamaw Desta, Kibrom Gebreselassie |
author_facet | Gebremariam, Dawit Seyoum Miruts, Asmamaw Desta, Kibrom Gebreselassie |
author_sort | Gebremariam, Dawit Seyoum |
collection | PubMed |
description | Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with other syndromes. Fetal sonographic diagnosis of this defect is possible, but less practiced. After birth, this defect can be easily diagnosed clinically because of the presence of paradoxical chest wall movement. The flexibility of the thorax is maximal and compression of the underlying structures is minimal during the neonatal and early infancy period, and this period is the preferred time for surgical repair. We report a 39-day-old infant who presented with an isolated V-shaped inferior sternal cleft, its surgical primary closure, and postoperative course. |
format | Online Article Text |
id | pubmed-9994661 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Dove |
record_format | MEDLINE/PubMed |
spelling | pubmed-99946612023-03-09 Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation Gebremariam, Dawit Seyoum Miruts, Asmamaw Desta, Kibrom Gebreselassie Pediatric Health Med Ther Case Report Sternal cleft is a rare chest wall anomaly resulting from a failure of the lateral mesodermal folds to migrate to the midline, causing a cleft in the early stage of embryological development. This can be a complete or partial defect. It can also occur as an isolated anomaly or in association with other syndromes. Fetal sonographic diagnosis of this defect is possible, but less practiced. After birth, this defect can be easily diagnosed clinically because of the presence of paradoxical chest wall movement. The flexibility of the thorax is maximal and compression of the underlying structures is minimal during the neonatal and early infancy period, and this period is the preferred time for surgical repair. We report a 39-day-old infant who presented with an isolated V-shaped inferior sternal cleft, its surgical primary closure, and postoperative course. Dove 2023-03-04 /pmc/articles/PMC9994661/ /pubmed/36910043 http://dx.doi.org/10.2147/PHMT.S397462 Text en © 2023 Gebremariam et al. https://creativecommons.org/licenses/by-nc/3.0/This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/ (https://creativecommons.org/licenses/by-nc/3.0/) ). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php). |
spellingShingle | Case Report Gebremariam, Dawit Seyoum Miruts, Asmamaw Desta, Kibrom Gebreselassie Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title | Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title_full | Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title_fullStr | Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title_full_unstemmed | Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title_short | Isolated V-Shaped Sternal Cleft — A Rare Chest Wall Malformation |
title_sort | isolated v-shaped sternal cleft — a rare chest wall malformation |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC9994661/ https://www.ncbi.nlm.nih.gov/pubmed/36910043 http://dx.doi.org/10.2147/PHMT.S397462 |
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