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Effects of CFTR modulators on serum biomarkers of liver fibrosis in children with cystic fibrosis

The cystic fibrosis (CF) transmembrane conductance regulator corrector/potentiator combinations lumacaftor/ivacaftor and elexacaftor/tezacaftor/ivacaftor improve sweat chloride, pulmonary function, and nutrition. Yet it is unclear whether they may also impact the progression of liver fibrosis, which...

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Detalles Bibliográficos
Autores principales:	Levitte, Steven, Fuchs, Yonathan, Wise, Russell, Sellers, Zachary M.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Lippincott Williams & Wilkins 2023
Materias:	Original Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10019140/ https://www.ncbi.nlm.nih.gov/pubmed/36662672 http://dx.doi.org/10.1097/HC9.0000000000000010

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