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Comparative analysis of right ventricular strain in Fabry cardiomyopathy and sarcomeric hypertrophic cardiomyopathy

AIMS: To perform a comparative analysis of right ventricle (RV) myocardial mechanics, assessed by 2D speckle-tracking echocardiography (2D-STE), between patients with Fabry disease and patients with sarcomeric disease. METHODS AND RESULTS: Patients with Fabry cardiomyopathy (FC) (n = 28) were compar...

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Detalles Bibliográficos
Autores principales: Meucci, Maria Chiara, Lillo, Rosa, Lombardo, Antonella, Lanza, Gaetano A, Bootsma, Marianne, Butcher, Steele C, Massetti, Massimo, Manna, Raffaele, Bax, Jeroen J, Crea, Filippo, Ajmone Marsan, Nina, Graziani, Francesca
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10029843/
https://www.ncbi.nlm.nih.gov/pubmed/35900225
http://dx.doi.org/10.1093/ehjci/jeac151