Beyond pigmentation: signs of liver protection during afamelanotide treatment in Swiss patients with erythropoietic protoporphyria, an observational study

Erythropoietic protoporphyria (EPP) is an ultra-rare inherited disorder with overproduction of protoporphyrin in maturating erythroblasts. This excess protoporphyrin leads to incapacitating phototoxic burns in sunlight exposed skin. Its biliary elimination causes cholestatic liver injury in 20% and...

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Detalles Bibliográficos
Autores principales: Minder, Anna-Elisabeth, Barman-Aksoezen, Jasmin, Schmid, Mathias, Minder, Elisabeth I., Zulewski, Henryk, Minder, Christoph E., Schneider-Yin, Xiaoye
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2021
Materias:
Original Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10032460/
https://www.ncbi.nlm.nih.gov/pubmed/37181106
http://dx.doi.org/10.1177/26330040211065453

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10032460/
https://www.ncbi.nlm.nih.gov/pubmed/37181106
http://dx.doi.org/10.1177/26330040211065453

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