AN 84-YEAR-OLD PATIENT WITH CAROLI SYNDROME: WHAT IS THE PROGNOSIS OF THIS CONDITION?

Caroli disease is a rare congenital pathology caused by mutation of the PKHD1 gene (polycystic kidney and hepatic disease 1), also responsible for autosomal recessive polycystic kidney disease. Characterized by segmental and multifocal dilatation of the large intrahepatic bile ducts, classic disease...

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Detalles Bibliográficos
Autores principales: Caleça Emidio, Fabio, Costa Pereira, Rafaela, Blanco, Rosário, Santos, Pedro, Abegão, Teresa, Fitas, Claudia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SMC Media Srl 2023
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10035612/
https://www.ncbi.nlm.nih.gov/pubmed/36969528
http://dx.doi.org/10.12890/2023_003794

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10035612/
https://www.ncbi.nlm.nih.gov/pubmed/36969528
http://dx.doi.org/10.12890/2023_003794

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