Cargando…
Endoscopic and Image Analysis of the Airway in Patients with Mucopolysaccharidosis Type IVA
Mucopolysaccharidosis (MPS) is a hereditary disorder arising from lysosomal enzymes deficiency, with glycosaminoglycans (GAGs) storage in connective tissues and bones, which may compromise the airway. This retrospective study evaluated patients with MPS type IVA with airway obstruction detected via...
Autores principales: | , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10059844/ https://www.ncbi.nlm.nih.gov/pubmed/36983675 http://dx.doi.org/10.3390/jpm13030494 |