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Endoscopic and Image Analysis of the Airway in Patients with Mucopolysaccharidosis Type IVA

Mucopolysaccharidosis (MPS) is a hereditary disorder arising from lysosomal enzymes deficiency, with glycosaminoglycans (GAGs) storage in connective tissues and bones, which may compromise the airway. This retrospective study evaluated patients with MPS type IVA with airway obstruction detected via...

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Detalles Bibliográficos
Autores principales:	Lee, Yi-Hao, Su, Chin-Hui, Lin, Che-Yi, Lin, Hsiang-Yu, Lin, Shuan-Pei, Chuang, Chih-Kuang, Lee, Kuo-Sheng
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10059844/ https://www.ncbi.nlm.nih.gov/pubmed/36983675 http://dx.doi.org/10.3390/jpm13030494

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