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Current clinical understanding and effectiveness of portopulmonary hypertension treatment

Portopulmonary hypertension (PoPH) is a rare subtype of Group 1 pulmonary arterial hypertension (PAH) with a poor prognosis. According to the most up-to-date definition, PoPH is characterized by a mean pulmonary arterial pressure (PAP) of >20 mmHg at rest, a pulmonary artery wedge pressure of ≤15...

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Detalles Bibliográficos
Autores principales: Tamura, Yuichi, Tamura, Yudai, Taniguchi, Yu, Atsukawa, Masanori
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10110923/
https://www.ncbi.nlm.nih.gov/pubmed/37081835
http://dx.doi.org/10.3389/fmed.2023.1142836