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CFTR function, pathology and pharmacology at single-molecule resolution

The cystic fibrosis transmembrane conductance regulator (CFTR) is an anion channel that regulates salt and fluid homeostasis across epithelial membranes(1). Alterations in CFTR cause cystic fibrosis, a fatal disease without a cure(2,3). Electrophysiological properties of CFTR have been analysed for...

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Detalles Bibliográficos
Autores principales: Levring, Jesper, Terry, Daniel S., Kilic, Zeliha, Fitzgerald, Gabriel, Blanchard, Scott C., Chen, Jue
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10115640/
https://www.ncbi.nlm.nih.gov/pubmed/36949202
http://dx.doi.org/10.1038/s41586-023-05854-7