Nanoscale Structural Comparison of Fibrillin-1 Microfibrils Isolated from Marfan and Non-Marfan Syndrome Human Aorta

Fibrillin-1 microfibrils are essential elements of the extracellular matrix serving as a scaffold for the deposition of elastin and endowing connective tissues with tensile strength and elasticity. Mutations in the fibrillin-1 gene (FBN1) are linked to Marfan syndrome (MFS), a systemic connective ti...

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Detalles Bibliográficos
Autores principales: Șulea, Cristina M., Mártonfalvi, Zsolt, Csányi, Csilla, Haluszka, Dóra, Pólos, Miklós, Ágg, Bence, Stengl, Roland, Benke, Kálmán, Szabolcs, Zoltán, Kellermayer, Miklós S. Z.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10145871/
https://www.ncbi.nlm.nih.gov/pubmed/37108724
http://dx.doi.org/10.3390/ijms24087561

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10145871/
https://www.ncbi.nlm.nih.gov/pubmed/37108724
http://dx.doi.org/10.3390/ijms24087561

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