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Tracheal Resection for Critical Airway Obstruction in Morquio A Syndrome

INTRODUCTION: The primary cause of death in Morquio A syndrome (mucopolysaccharidosis (MPS) IVA) is airway obstruction, brought about by an inexorable and pathognomonic multilevel airway tortuosity, buckling, and obstruction. The relative pathophysiological contributions of an inherent cartilage pro...

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Detalles Bibliográficos
Autores principales: Frauenfelder, Claire, Maughan, Elizabeth, Kenth, Johnny, Nandi, Reema, Jones, Simon, Walker, Robert, Walsh, Bill, Muthialu, Nagarajan, Bruce, Iain, Hewitt, Richard, Butler, Colin
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10171972/
https://www.ncbi.nlm.nih.gov/pubmed/37180285
http://dx.doi.org/10.1155/2023/7976780