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Idiopathic pulmonary fibrosis and the role of genetics in the era of precision medicine

Idiopathic pulmonary fibrosis (IPF) is a chronic, rare progressive lung disease, characterized by lung scarring and the irreversible loss of lung function. Two anti-fibrotic drugs, nintedanib and pirfenidone, have been demonstrated to slow down disease progression, although IPF mortality remains a c...

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Detalles Bibliográficos
Autores principales: Alonso-Gonzalez, Aitana, Tosco-Herrera, Eva, Molina-Molina, Maria, Flores, Carlos
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10172674/
https://www.ncbi.nlm.nih.gov/pubmed/37181377
http://dx.doi.org/10.3389/fmed.2023.1152211