Clinical Manifestations, Current and Future Therapy, and Long-Term Outcomes in Congenital Thrombotic Thrombocytopenic Purpura

Congenital thrombotic thrombocytopenic purpura (cTTP) is an extremely rare disease characterized by the severe deficiency of a disintegrin and metalloproteinase with thrombospondin type 1 motifs 13 (ADAMTS13), caused by ADAMTS13 mutations. While ADAMTS13 supplementation by fresh frozen plasma (FFP)...

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Detalles Bibliográficos
Autores principales: Sakai, Kazuya, Matsumoto, Masanori
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10219024/
https://www.ncbi.nlm.nih.gov/pubmed/37240470
http://dx.doi.org/10.3390/jcm12103365

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10219024/
https://www.ncbi.nlm.nih.gov/pubmed/37240470
http://dx.doi.org/10.3390/jcm12103365

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