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Outcomes from a Single Transplant Center of 5 Pediatric Cases of Domino Liver Transplantation from Live Donors with Maple Syrup Urine Disease

BACKGROUND: Maple syrup urine disease (MSUD) is a rare genetic deficiency of the branched-chain α-keto acid dehydrogenase (BCKAD) complex that breaks down amino acids, resulting in multi-organ failure. This report is of 5 pediatric cases of domino liver transplantation (DLT) from live donors with MS...

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Detalles Bibliográficos
Autores principales: Zhang, Jin-Ping, Zhu, Zhi-Jun, Sun, Li-Ying, Wei, Lin, Qu, Wei, Zeng, Zhi-Gui, Zhang, Hai-Ming, Liu, Ying
Formato: Online Artículo Texto
Lenguaje:English
Publicado: International Scientific Literature, Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10239205/
https://www.ncbi.nlm.nih.gov/pubmed/37248682
http://dx.doi.org/10.12659/AOT.939893