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Aspartame and Phenylketonuria: an analysis of the daily phenylalanine intake of aspartame-containing drugs marketed in France

BACKGROUND: Phenylketonuria (PKU) is a rare genetic metabolic disorder in which especially high phenylalanine (Phe) concentrations cause brain dysfunction. If untreated, this brain dysfunction results in severe microcephaly, intellectual disability, and behavioral problems. Dietary restriction of Ph...

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Detalles Bibliográficos
Autores principales: Maler, Victor, Goetz, Violette, Tardieu, Marine, Khalil, Abderrahmane El, Alili, Jean Meidi, Meunier, Philippe, Maillot, François, Labarthe, François
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10249154/
https://www.ncbi.nlm.nih.gov/pubmed/37291632
http://dx.doi.org/10.1186/s13023-023-02770-x