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DICER1 Syndrome: A Multicenter Surgical Experience and Systematic Review

SIMPLE SUMMARY: DICER1 syndrome is a rare genetic disorder that predisposes patients to the development of malignant and non-malignant diseases. Currently, DICER1 syndrome diagnosis still occurs late, usually following surgical operations, affecting patients’ outcomes, especially for further neoplas...

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Detalles Bibliográficos
Autores principales: Spinelli, Claudio, Ghionzoli, Marco, Sahli, Linda Idrissi, Guglielmo, Carla, Frascella, Silvia, Romano, Silvia, Ferrari, Carlo, Gennari, Fabrizio, Conzo, Giovanni, Morganti, Riccardo, De Napoli, Luigi, Quaglietta, Lucia, De Martino, Lucia, Picariello, Stefania, Grandone, Anna, Luongo, Caterina, Gambale, Antonella, Patrizio, Armando, Fallahi, Poupak, Antonelli, Alessandro, Ferrari, Silvia Martina
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10377723/
https://www.ncbi.nlm.nih.gov/pubmed/37509342
http://dx.doi.org/10.3390/cancers15143681