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Mucolytic treatment of chronic rhinosinusitis in a murine model of primary ciliary dyskinesia

Background: Genetic defects in motile cilia cause primary ciliary dyskinesia (PCD), a rare disease with no specific therapeutics. Individuals with PCD often have impaired fertility and laterality defects and universally suffer from upper and lower airway diseases. Chronic rhinosinusitis is a univers...

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Detalles Bibliográficos
Autores principales: Yin, Weining, Golliher, Hannah L., Ferguson, Amy J., Kimbell, Julia S., Livraghi-Butrico, Alessandra, Rogers, Troy D., Grubb, Barbara R., Kimple, Adam J., Ostrowski, Lawrence E.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10405821/
https://www.ncbi.nlm.nih.gov/pubmed/37555015
http://dx.doi.org/10.3389/fmolb.2023.1221796