Unexpected sirolimus-stimulated airway hyperreactivity in lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a multisystem disease affecting primarily women, characterised in the lung by proliferation of LAM cells, abnormal smooth muscle-like cells with dysfunctional tuberous sclerosis complex genes. This dysfunction results in activation of mechanistic target of rapamycin...

Descripción completa

Detalles Bibliográficos
Autores principales: Steagall, Wendy K., Stylianou, Mario, Pacheco-Rodriguez, Gustavo, Yu, Zu Xi, Moss, Joel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2023
Materias:
Research Letters
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10423980/
https://www.ncbi.nlm.nih.gov/pubmed/37589458
http://dx.doi.org/10.1183/23120541.00305-2023

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10423980/
https://www.ncbi.nlm.nih.gov/pubmed/37589458
http://dx.doi.org/10.1183/23120541.00305-2023

Ejemplares similares