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Unexpected sirolimus-stimulated airway hyperreactivity in lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a multisystem disease affecting primarily women, characterised in the lung by proliferation of LAM cells, abnormal smooth muscle-like cells with dysfunctional tuberous sclerosis complex genes. This dysfunction results in activation of mechanistic target of rapamycin...

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Detalles Bibliográficos
Autores principales:	Steagall, Wendy K., Stylianou, Mario, Pacheco-Rodriguez, Gustavo, Yu, Zu Xi, Moss, Joel
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	European Respiratory Society 2023
Materias:	Research Letters
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10423980/ https://www.ncbi.nlm.nih.gov/pubmed/37589458 http://dx.doi.org/10.1183/23120541.00305-2023

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