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Platelet functional abnormalities in pediatric patients with kaposiform hemangioendothelioma/Kasabach-Merritt phenomenon
Kaposiform hemangioendothelioma (KHE) is a rare vascular tumor of infancy that is commonly associated with a life-threatening thrombocytopenic condition, Kasabach-Merritt phenomenon (KMP). Platelet CLEC-2, tumor podoplanin interaction is considered the key mechanism of platelet clearance in these pa...
Autores principales: | Martyanov, Alexey A., Tesakov, Ivan P., Khachatryan, Lili A., An, Olga I., Boldova, Anna E., Ignatova, Anastasia A., Koltsova, Ekaterina M., Korobkin, Julia-Jessica D., Podoplelova, Nadezhda A., Svidelskaya, Galina S., Yushkova, Eugenia, Novichkova, Galina A., Eble, Johannes A., Panteleev, Mikhail A., Kalinin, Dmitrii V., Sveshnikova, Anastasia N. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The American Society of Hematology
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10463204/ https://www.ncbi.nlm.nih.gov/pubmed/37307200 http://dx.doi.org/10.1182/bloodadvances.2022009590 |
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