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Metabolic switch from fatty acid oxidation to glycolysis in knock‐in mouse model of Barth syndrome

Mitochondria are central for cellular metabolism and energy supply. Barth syndrome (BTHS) is a severe disorder, due to dysfunction of the mitochondrial cardiolipin acyl transferase tafazzin. Altered cardiolipin remodeling affects mitochondrial inner membrane organization and function of membrane pro...

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Detalles Bibliográficos
Autores principales: Chowdhury, Arpita, Boshnakovska, Angela, Aich, Abhishek, Methi, Aditi, Vergel Leon, Ana Maria, Silbern, Ivan, Lüchtenborg, Christian, Cyganek, Lukas, Prochazka, Jan, Sedlacek, Radislav, Lindovsky, Jiri, Wachs, Dominic, Nichtova, Zuzana, Zudova, Dagmar, Koubkova, Gizela, Fischer, André, Urlaub, Henning, Brügger, Britta, Katschinski, Dörthe M, Dudek, Jan, Rehling, Peter
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10493589/
https://www.ncbi.nlm.nih.gov/pubmed/37533404
http://dx.doi.org/10.15252/emmm.202317399