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Cell-type-specific disruption of cortico-striatal circuitry drives repetitive patterns of behavior in fragile X syndrome model mice

Individuals with fragile X syndrome (FXS) are frequently diagnosed with autism spectrum disorder (ASD), including increased risk for restricted and repetitive behaviors (RRBs). Consistent with observations in humans, FXS model mice display distinct RRBs and hyperactivity that are consistent with dys...

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Detalles Bibliográficos
Autores principales: Longo, Francesco, Aryal, Sameer, Anastasiades, Paul G., Maltese, Marta, Baimel, Corey, Albanese, Federica, Tabor, Joanna, Zhu, Jeffrey D., Oliveira, Mauricio M., Gastaldo, Denise, Bagni, Claudia, Santini, Emanuela, Tritsch, Nicolas X., Carter, Adam G., Klann, Eric
Formato: Online Artículo Texto
Lenguaje:English
Publicado: 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10552611/
https://www.ncbi.nlm.nih.gov/pubmed/37505982
http://dx.doi.org/10.1016/j.celrep.2023.112901