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Effective Long-term Pediatric Pegvisomant Monotherapy to Final Height in X-linked Acrogigantism
X-linked acrogigantism (X-LAG) is characterized by extreme tall stature from early childhood resulting from duplication of the GPR101 gene, in turn resulting in GH excess. Most cases present with pituitary tumors secreting GH and prolactin. Diffuse pituitary hyperplasia is uncommon and normal prolac...
Autores principales: | Burren, Christine P, Williams, Georgina, Coxson, Edward, Korbonits, Márta |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10580488/ https://www.ncbi.nlm.nih.gov/pubmed/37908565 http://dx.doi.org/10.1210/jcemcr/luad028 |
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