A very rare cause of pre‐capillary pulmonary hypertension: The PAMI syndrome

We report the first known case of PAMI syndrome associated with pulmonary arterial hypertension (PAH) with a positive response to cyclophosphamide and pulmonary vasodilators. The patient's history began at 7 months with severe pancytopenia and fever. As time progressed, migrating arthritis, hep...

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Detalles Bibliográficos
Autores principales: Iseppi, Manuela, Savonitto, Giulio, Tommasini, Alberto, Pin, Alessia, Sinagra, Gianfranco, Stolfo, Davide
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10590960/
https://www.ncbi.nlm.nih.gov/pubmed/37876942
http://dx.doi.org/10.1002/pul2.12300

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10590960/
https://www.ncbi.nlm.nih.gov/pubmed/37876942
http://dx.doi.org/10.1002/pul2.12300

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