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A very rare cause of pre‐capillary pulmonary hypertension: The PAMI syndrome

We report the first known case of PAMI syndrome associated with pulmonary arterial hypertension (PAH) with a positive response to cyclophosphamide and pulmonary vasodilators. The patient's history began at 7 months with severe pancytopenia and fever. As time progressed, migrating arthritis, hep...

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Detalles Bibliográficos
Autores principales:	Iseppi, Manuela, Savonitto, Giulio, Tommasini, Alberto, Pin, Alessia, Sinagra, Gianfranco, Stolfo, Davide
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2023
Materias:	Case Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10590960/ https://www.ncbi.nlm.nih.gov/pubmed/37876942 http://dx.doi.org/10.1002/pul2.12300

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