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Congenital Hepatic Fibrosis in a 2-Year-Old Child Presenting with Fever of Unknown Origin

Congenital hepatic fibrosis is a rare, autosomal recessive, fibro-polycystic disease resulting from ductal plate malformation, leading to proliferation and fibrosis of bile ducts. Progressive hepatic fibrosis leads to portal hypertension and varices which can present with life threatening gastrointe...

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Detalles Bibliográficos
Autores principales: Penfold, Michael P., Annankra, Wentiirim B., Hull, Nathan C., Corredor, Margarita
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10632057/
https://www.ncbi.nlm.nih.gov/pubmed/37946748
http://dx.doi.org/10.1155/2023/4497784