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Congenital Hepatic Fibrosis in a 2-Year-Old Child Presenting with Fever of Unknown Origin
Congenital hepatic fibrosis is a rare, autosomal recessive, fibro-polycystic disease resulting from ductal plate malformation, leading to proliferation and fibrosis of bile ducts. Progressive hepatic fibrosis leads to portal hypertension and varices which can present with life threatening gastrointe...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Hindawi
2023
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10632057/ https://www.ncbi.nlm.nih.gov/pubmed/37946748 http://dx.doi.org/10.1155/2023/4497784 |