Impact of enzyme replacement therapy and migalastat on left atrial strain and cardiomyopathy in patients with Fabry disease

AIMS: Cardiomyopathy in Fabry disease (FD) is a major determinant of morbidity and mortality. This study investigates the effects of FD-specific treatment using enzyme replacement therapy (ERT) and chaperone therapy on left atrial (LA) function using two-dimensional speckle tracking echocardiography...

Descripción completa

Detalles Bibliográficos
Autores principales: Pogoda, Christian, Brand, Stefan-Martin, Duning, Thomas, Schmidt-Pogoda, Antje, Sindermann, Jürgen, Lenders, Malte, Brand, Eva
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10656767/
https://www.ncbi.nlm.nih.gov/pubmed/38028489
http://dx.doi.org/10.3389/fcvm.2023.1223635