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Impact of enzyme replacement therapy and migalastat on left atrial strain and cardiomyopathy in patients with Fabry disease
AIMS: Cardiomyopathy in Fabry disease (FD) is a major determinant of morbidity and mortality. This study investigates the effects of FD-specific treatment using enzyme replacement therapy (ERT) and chaperone therapy on left atrial (LA) function using two-dimensional speckle tracking echocardiography...
Autores principales: | Pogoda, Christian, Brand, Stefan-Martin, Duning, Thomas, Schmidt-Pogoda, Antje, Sindermann, Jürgen, Lenders, Malte, Brand, Eva |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10656767/ https://www.ncbi.nlm.nih.gov/pubmed/38028489 http://dx.doi.org/10.3389/fcvm.2023.1223635 |
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