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Adherent Monomer-Misfolded SOD1

BACKGROUND: Multiple cellular functions are compromised in amyotrophic lateral sclerosis (ALS). In familial ALS (FALS) with Cu/Zn superoxide dismutase (SOD1) mutations, the mechanisms by which the mutation in SOD1 leads to such a wide range of abnormalities remains elusive. METHODOLOGY/PRINCIPAL FIN...

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Detalles Bibliográficos
Autores principales: Watanabe, Yasuhiro, Morita, Eri, Fukada, Yasuyo, Doi, Koji, Yasui, Kenichi, Kitayama, Michio, Nakano, Toshiya, Nakashima, Kenji
Formato: Texto
Lenguaje:English
Publicado: Public Library of Science 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2567031/
https://www.ncbi.nlm.nih.gov/pubmed/18946506
http://dx.doi.org/10.1371/journal.pone.0003497