Familial pulmonary alveolar proteinosis caused by mutations in CSF2RA

Primary pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by accumulation of surfactant in the lungs that is presumed to be mediated by disruption of granulocyte/macrophage colony-stimulating factor (GM-CSF) signaling based on studies in genetically modified mice. The effects of...

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Detalles Bibliográficos
Autores principales: Suzuki, Takuji, Sakagami, Takuro, Rubin, Bruce K., Nogee, Lawrence M., Wood, Robert E., Zimmerman, Sarah L., Smolarek, Teresa, Dishop, Megan K., Wert, Susan E., Whitsett, Jeffrey A., Grabowski, Gregory, Carey, Brenna C., Stevens, Carrie, van der Loo, Johannes C.M., Trapnell, Bruce C.
Formato: Texto
Lenguaje:English
Publicado: The Rockefeller University Press 2008
Materias:
Brief Definitive Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2585845/
https://www.ncbi.nlm.nih.gov/pubmed/18955570
http://dx.doi.org/10.1084/jem.20080990

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2585845/
https://www.ncbi.nlm.nih.gov/pubmed/18955570
http://dx.doi.org/10.1084/jem.20080990

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