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A Case of Fabry Cardiomyopathy

In the absence of hypertension, hypertrophic cardiomyopathy is the most common cause of left ventricular hypertrophy (LVH). However, it has been reported that up to 3% of males with unexplained LVH have Fabry disease, an X-linked disorder of glycophospholipid metabolism that is due to a deficiency i...

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Detalles Bibliográficos
Autores principales: Nah, Jong Chun, Kim, Woo-Shik, Cho, Wook-Hyun, Choi, Suk-Koo, Yoo, Han-Wook, Takenaka, Toshihiro, Tei, Chuwa
Formato: Texto
Lenguaje:English
Publicado: The Korean Society of Cardiology 2009
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2771845/
https://www.ncbi.nlm.nih.gov/pubmed/19949640
http://dx.doi.org/10.4070/kcj.2009.39.8.335