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Frequency of ubiquitin and FUS-positive, TDP-43-negative frontotemporal lobar degeneration

Frontotemporal lobar degeneration (FTLD) is a clinically, genetically and pathologically heterogeneous disorder. Within FTLD with ubiquitin-positive inclusions (FTLD-U), a new pathological subtype named FTLD-FUS was recently found with fused in sarcoma (FUS) positive, TDP-43-negative inclusions, and...

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Detalles Bibliográficos
Autores principales: Seelaar, Harro, Klijnsma, Kirsten Y., de Koning, Inge, van der Lugt, Aad, Chiu, Wang Zheng, Azmani, Asma, Rozemuller, Annemieke J. M., van Swieten, John C.
Formato: Texto
Lenguaje:English
Publicado: Springer-Verlag 2009
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2864899/
https://www.ncbi.nlm.nih.gov/pubmed/19946779
http://dx.doi.org/10.1007/s00415-009-5404-z