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Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report

Background. Cutis laxa (CL) is a rare disorder of elastic tissue characterized by loose, sagging skin with reduced elasticity, and resilience without resulting scarring. CL may be inherited as a dominant, recessive, or X-linked recessive disease, or acquired. The heritable forms of CL predominantly...

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Autores principales: Gverić, Tugomir, Barić, Marko, Bulat, Vedrana, Šitum, Mirna, Pušić, Jana, Huljev, Dubravko, Zdilar, Boris, Gverić-Ahmetašević, Snježana, Tomas, Davor
Formato: Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2879976/
https://www.ncbi.nlm.nih.gov/pubmed/20585600
http://dx.doi.org/10.1155/2010/402093
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author Gverić, Tugomir
Barić, Marko
Bulat, Vedrana
Šitum, Mirna
Pušić, Jana
Huljev, Dubravko
Zdilar, Boris
Gverić-Ahmetašević, Snježana
Tomas, Davor
author_facet Gverić, Tugomir
Barić, Marko
Bulat, Vedrana
Šitum, Mirna
Pušić, Jana
Huljev, Dubravko
Zdilar, Boris
Gverić-Ahmetašević, Snježana
Tomas, Davor
author_sort Gverić, Tugomir
collection PubMed
description Background. Cutis laxa (CL) is a rare disorder of elastic tissue characterized by loose, sagging skin with reduced elasticity, and resilience without resulting scarring. CL may be inherited as a dominant, recessive, or X-linked recessive disease, or acquired. The heritable forms of CL predominantly begin at birth, but it may be delayed until puberty or age of 30 years with extracutaneous manifestations including pulmonary emphysema, umbilical and inguinal hernias, and gastrointestinal and vesicourinary tract diverticuli. An acquired form of the disease occurs in adults with no evidence of internal organ involvement. Objective. The aim of this case report was to present our patient suffering from CL, and to evaluate clinical presentation, diagnostic and therapeutic difficulties in this rare condition. Case Report. A 30-year-old female patient was admitted to our Hospital due to localized loose and sagging skin of abdomen, induced by prior cesarean section 6 years ago. CL has been diagnosed based on the clinical picture and pathohistological appearance. Conclusion. Reconstructive surgery provides a dramatic cosmetic improvement with significant psychosocial benefit. Repeated surgical procedures may be required to correct the lax skin, which worsens with age.
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spelling pubmed-28799762010-06-28 Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report Gverić, Tugomir Barić, Marko Bulat, Vedrana Šitum, Mirna Pušić, Jana Huljev, Dubravko Zdilar, Boris Gverić-Ahmetašević, Snježana Tomas, Davor Dermatol Res Pract Case Report Background. Cutis laxa (CL) is a rare disorder of elastic tissue characterized by loose, sagging skin with reduced elasticity, and resilience without resulting scarring. CL may be inherited as a dominant, recessive, or X-linked recessive disease, or acquired. The heritable forms of CL predominantly begin at birth, but it may be delayed until puberty or age of 30 years with extracutaneous manifestations including pulmonary emphysema, umbilical and inguinal hernias, and gastrointestinal and vesicourinary tract diverticuli. An acquired form of the disease occurs in adults with no evidence of internal organ involvement. Objective. The aim of this case report was to present our patient suffering from CL, and to evaluate clinical presentation, diagnostic and therapeutic difficulties in this rare condition. Case Report. A 30-year-old female patient was admitted to our Hospital due to localized loose and sagging skin of abdomen, induced by prior cesarean section 6 years ago. CL has been diagnosed based on the clinical picture and pathohistological appearance. Conclusion. Reconstructive surgery provides a dramatic cosmetic improvement with significant psychosocial benefit. Repeated surgical procedures may be required to correct the lax skin, which worsens with age. Hindawi Publishing Corporation 2010 2010-03-04 /pmc/articles/PMC2879976/ /pubmed/20585600 http://dx.doi.org/10.1155/2010/402093 Text en Copyright © 2010 Tugomir Gverić et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Gverić, Tugomir
Barić, Marko
Bulat, Vedrana
Šitum, Mirna
Pušić, Jana
Huljev, Dubravko
Zdilar, Boris
Gverić-Ahmetašević, Snježana
Tomas, Davor
Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title_full Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title_fullStr Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title_full_unstemmed Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title_short Clinical Presentation of a Patient with Localized Acquired Cutis Laxa of Abdomen: A Case Report
title_sort clinical presentation of a patient with localized acquired cutis laxa of abdomen: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2879976/
https://www.ncbi.nlm.nih.gov/pubmed/20585600
http://dx.doi.org/10.1155/2010/402093
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