Histochemical and cellular changes accompanying the appearance of lung fibrosis in an experimental mouse model for Hermansky Pudlak syndrome

Hermansky Pudlak syndrome (HPS) is a heterogeneous recessive genetic disease with a tendency to develop lung fibrosis with aging. A mouse strain with two mutant HPS genes affecting separate vesicle trafficking pathways, C57BL/6-Hps1 (ep)-Ap3b1 (pe), exhibits severe lung abnormalities at young ages,...

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Detalles Bibliográficos
Autores principales: Wang, Lingyan, Lyerla, Timothy
Formato: Texto
Lenguaje:English
Publicado: Springer-Verlag 2010
Materias:
Original Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2909458/
https://www.ncbi.nlm.nih.gov/pubmed/20603711
http://dx.doi.org/10.1007/s00418-010-0724-8

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2909458/
https://www.ncbi.nlm.nih.gov/pubmed/20603711
http://dx.doi.org/10.1007/s00418-010-0724-8

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