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Intensive care management of patients with acute intermittent porphyria: Clinical report of four cases and review of literature

Acute intermittent porphyria (AIP), the most common and the most severe form of acute hepatic porphyria, is an autosomal dominant condition. It results from lower-than-normal levels (less than 50%) of porphobilinogen (PBG) deaminase. Patients may present commonly with gastrointestinal complaints and...

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Detalles Bibliográficos
Autores principales: Mehta, Madhur, Rath, Girija P., Padhy, Uma P., Marda, Manish, Mahajan, Charu, Dash, Hari H.
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2936738/
https://www.ncbi.nlm.nih.gov/pubmed/20859493
http://dx.doi.org/10.4103/0972-5229.68222