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The Δ4-desaturation pathway for DHA biosynthesis is operative in the human species: Differences between normal controls and children with the Zellweger syndrome
BACKGROUND: Docosahexaenoic acid (DHA, 22:6ω3) is a fundamental component of cell membranes, especially in the brain and retina. In the experimental animal, DHA deficiency leads to suboptimal neurological performance and visual deficiencies. Children with the Zellweger syndrome (ZS) have a profound...
Autores principales: | Martinez, Manuela, Ichaso, Natalia, Setien, Fernando, Durany, Nuria, Qiu, Xiao, Roesler, William |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2949860/ https://www.ncbi.nlm.nih.gov/pubmed/20828389 http://dx.doi.org/10.1186/1476-511X-9-98 |
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